Primary anaplastic large cell lymphoma of the pancreas

Authors

Keywords:

anaplastic lymphoma kinase, lymphoma, pancreas.

Abstract

Introduction: Primary pancreatic anaplastic large cell lymphoma is a very rare entity and only 13 cases have been described in the literature.
Objectives: To present a rare clinical case of anaplastic large cell lymphoma negative for anaplastic lymphoma kinase and with extranodal presentation in the gastrointestinal tract.
Clinical case: An 80-year-old male patient presented with abdominal pain, regurgitation, jaundice, and weight loss. Abdominal CT showed a mass in the head of the pancreas extending to segment V of the liver, accompanied by mesenteric and retroperitoneal adenopathy. Biopsy of the lesion was consistent with anaplastic lymphoma kinase-negative anaplastic large cell lymphoma. Mini-CHOP was indicated for 1 cycle. The patient subsequently developed neutropenic sepsis and died 3 months after diagnosis.
Conclusions: Anaplastic lymphoma kinase-negative anaplastic large cell lymphoma is a rare entity whose extranodal localization, particularly in the gastrointestinal tract, is uncommon.

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References

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Published

2024-11-30

How to Cite

1.
Beltrán Gárate B, Alburqueque-Melgarejo J, Villela L, De la Cruz-Vargas JA. Primary anaplastic large cell lymphoma of the pancreas. Rev Cubana Med Milit [Internet]. 2024 Nov. 30 [cited 2025 Apr. 3];53(4):e024066724. Available from: https://revmedmilitar.sld.cu/index.php/mil/article/view/66724

Issue

Vol. 53 No. 4 (2024): October - December

Section

Case Presentation

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