Manejo ventilatorio no invasivo de un paciente con enfermedad de Steinert
Abstract
Introducción: la enfermedad de Steinert es una enfermedad neuromuscular crónica y progresiva de carácter autosómico dominante. Debido a que puede afectar a los músculos respiratorios, los pacientes se benefician de distintas técnicas de fisioterapia con el fin de evitar complicaciones.
Caso clínico: paciente con enfermedad de Steinert que fue tratada en un hospital público de la provincia de Buenos Aires durante un cuadro de insuficiencia respiratoria aguda, de manera no invasiva.
Comentarios: esta experiencia muestra que estos pacientes pueden ser tratados de manera no invasiva, fuera de la unidad de cuidados intensivos, y ser controlados ambulatoriamente luego de su egreso pudiendo reinsertarse en la comunidad. Asimismo, cabe destacar que esto fue posible en un hospital público, dentro de un contexto institucional y socioeconómico desfavorable.
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References
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4. Farrero E, Antón A, Egea CJ, Almaraz MJ, Masa JF, Utrabo I, et al. Normativa sobre el manejo de las complicaciones respiratorias de los pacientes con enfermedad neuromuscular (SEPAR). Arch Bonconeumol. 2013; 49(7):306-313.
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7. Prado F, Salinas P, Zenteno D, Vera R, Flores E, García C, et al. Recomendaciones para los cuidados respiratorios del niño y adolescente con enfermedades neuromusculares. Neumol Pediatr 2010; 5: 74-88.
8. Ambrosino N, Carpenè, Gherardi M. Chronic respiratory care for neuromuscular diseases in adults. Review. EurRespir J 2009; 34: 444-451.
9. Bach JR. Mechanical lnsufflation-Exsufflation. Comparison of Peak Expiratory Flows with Manually Assisted and Unassisted Coughing Techniques.Chest 1993; 104:1553-62.
10. Winck JC, Gonçalves MR, Lourenço C, Viana P, Almeida J, Bach JR. Effects of Mechanical Insufflation Exsufflation on Respiratory Parameters for Patients With Chronic Airway Secretion Encumbrance. CHEST 2004; 126:774-780.
11. Bach JR, Gonçalves MR, Hon A, Ishikawa Y, De Vito EL, Prado F, et al. Changing Trends in the Management of End-Stage Neuromuscular Respiratory Muscle Failure Recommendations of an International Consensus. Am J Phys Med Rehabil 2012; 91:00-00.
12. Johns MW. A new method for measuring daytime slepiness: the Epworth sleepines scale. Sleep 1991;14:50-5.
13. Bach JR, Mahajan K, Lipa B, Saporito L, Goncalves M, Komaroff E. Lung Insufflation Capacity in Neuromuscular Disease. Am J Phys Med Rehabil 2008; 87:720-725.
14. Tzeng AC, Bach JR. Prevention of Pulmonary Morbidity for Patients With Neuromuscular Disease. CHEST 2000; 118:1390-1396.
2. Thurner C, Hilton J. The myotonic dystrophies: diagnosis and managment. J Neurol Neurosurg Psychiatry. 2010 Apr 81(4):358-67.
3. Dominguez Flores ME, Luna Padrón E, Peñalosa Ochoa L,Galicia Amor S, Toral Freyre S, Baños Mejía BO, et al. Guía para el diagnóstico y tratamiento de las alteraciones respiratorias en las enfermedades neuromusculares. Neumolcir torax 2011; 70(1):5-70.
4. Farrero E, Antón A, Egea CJ, Almaraz MJ, Masa JF, Utrabo I, et al. Normativa sobre el manejo de las complicaciones respiratorias de los pacientes con enfermedad neuromuscular (SEPAR). Arch Bonconeumol. 2013; 49(7):306-313.
5. Aruj PK, Monteiro SG, De Vito EL. Análisis de factores relacionados con hipercapnia crónica en la distrofia miotónica. Medicina (Buenos Aires) 2013; 73: 529-534.
6. Panitch HB. Respiratory issues in the management of children with Neuromuscular Disease. Respir Care 2006; 51(8):885-893.
7. Prado F, Salinas P, Zenteno D, Vera R, Flores E, García C, et al. Recomendaciones para los cuidados respiratorios del niño y adolescente con enfermedades neuromusculares. Neumol Pediatr 2010; 5: 74-88.
8. Ambrosino N, Carpenè, Gherardi M. Chronic respiratory care for neuromuscular diseases in adults. Review. EurRespir J 2009; 34: 444-451.
9. Bach JR. Mechanical lnsufflation-Exsufflation. Comparison of Peak Expiratory Flows with Manually Assisted and Unassisted Coughing Techniques.Chest 1993; 104:1553-62.
10. Winck JC, Gonçalves MR, Lourenço C, Viana P, Almeida J, Bach JR. Effects of Mechanical Insufflation Exsufflation on Respiratory Parameters for Patients With Chronic Airway Secretion Encumbrance. CHEST 2004; 126:774-780.
11. Bach JR, Gonçalves MR, Hon A, Ishikawa Y, De Vito EL, Prado F, et al. Changing Trends in the Management of End-Stage Neuromuscular Respiratory Muscle Failure Recommendations of an International Consensus. Am J Phys Med Rehabil 2012; 91:00-00.
12. Johns MW. A new method for measuring daytime slepiness: the Epworth sleepines scale. Sleep 1991;14:50-5.
13. Bach JR, Mahajan K, Lipa B, Saporito L, Goncalves M, Komaroff E. Lung Insufflation Capacity in Neuromuscular Disease. Am J Phys Med Rehabil 2008; 87:720-725.
14. Tzeng AC, Bach JR. Prevention of Pulmonary Morbidity for Patients With Neuromuscular Disease. CHEST 2000; 118:1390-1396.
Published
2017-12-07
How to Cite
1.
Herrero MV, Faggionato M, Cigarra C, Rigoni L, de la Cruz M. Manejo ventilatorio no invasivo de un paciente con enfermedad de Steinert. Rev Cubana Med Milit [Internet]. 2017 Dec. 7 [cited 2025 Jan. 9];46(4). Available from: https://revmedmilitar.sld.cu/index.php/mil/article/view/42
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